PRUNE BELLY SYNDROME ASSOCIATED WITH BILATERAL MULTICYSTIC DYSPLASTIC KIDNEYS AND URETHRAL OBSTRUCTION: A CASE REPORT

Abstract

Arzu Akdag, Sule Arici, Betul Orhaner, Anil Dogan

Prune belly syndrome is a rare congenital disorder defined by a characteristic clinical triad: Abdominal muscle deficiency, severe urinary tract abnormalities,and bilateral cryptorchidism. We describe a preterm neonate of Prune Bellysyndrome who had abdominal muscle deficiency, multicystic dysplastic kidney,urethral hypoplasia and pulmonary hypoplasia. We presented this rare case withthe data gathered from the literature.